Creutzfeldt-Jakob Disease (=CJD) is a prion disease which causes a rapidly progressive dementia with myoclonus.
The majority of cases are sporadic. There is also an inherited form and an acquired form (=varient CJD, from meat infected with BSE)
CSF examination is usually normal but EEG shows characteristic biphasic high-amplitude sharp waves.
Death is usually within 6 months.
On a lighter note lets look at herpes zoster opthalmicus...