- cerebellum (may present as ataxia)
- spinal cord
- retina (may present as visual loss)
It is associated with bilateral renal cell carcinomas (develop in approximately 50% of patients with VHL) and pheochromocytomas.
For those of you who are feeling really geeky the gene responsible is on chromosome 3 and it is a mutation in a tumour supressor gene.
So after that brief acquaintance, lets move on to a condition I'd never heard of before today - neuralgic amyotrophy...